Unilateral Nevoid Telengiectasia

Abstract

Unilateral nevoid telangiectasia is a disease in which fine telangiectasia develop in a unilateral, sometimes dermatomal distribution. This disease was first described by Blascho in 1899 and there have been fewer than 100 reported cases heretofore. Unilateral nevoid telangiectasia may be congenital or acquired. Whereas congenital forms mainly seen in men, acquired forms seen in female. However etiopathogenesis is still uncertain, high estrogen levels may be responsible in women. Herein, we present a 40 year-old female patient with a diagnosis of acquired unilateral nevoid telangiectasia involving C3 dermatome and mandibular branch of trigeminal nerve with normal estrogen levels.