Cutaneous T cell lymphoma in a patient with primary biliary cholangitis

Abstract

Primary biliary cholangitis (PBC) is an autoimmune and cholestatic, liver disease characterized by chronic nonsuppurative destructive cholangitis, circulating antimitochondrial antibodies and interlobular bile duct destruction. Autoimmune disorders including PBC seems to have an elevated risk of lymphoma. Mycosis Fungoides, the most common type of Cutaneous T- cell lymphoma (CTCL) is also a neoplasm of the immune system. There is little information about the risk of developing lymphoma including CTCL in PBC patients. Here, we present the second case of CTCL as much as we know, reported in the literature that occurred in an adult patient with PBC. Copyright © 2017 by Türkiye Klinikleri.