Intrathoracic malignant peripheral nerve sheath tumor with angtosarcoma in a child with NF1
Tarih
2007Yazar
Elli, MuratCan, Bilge
Ceyhan, Meltem
Pinarli, Faruk Gueclue
Dagdemir, Ayhan
Ayyildiz, Halil Suat
Dagcinar, Adnan
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Tüm öğe kaydını gösterÖzet
Malignant peripheral nerve sheath tumors (MPNSTs) are uncommon in children and adolescents but occur more frequently in NF1 patients. Angiosarcomatous differentiation in MPNSTs is a rare entity with poor prognosis. We report on a 13-year-old boy with intrathoracic angiosarcoma arising in MPNST associated with NF1.